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KMID : 0371320060700010065
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Journal of the Korean Surgical Society
2006 Volume.70 No. 1 p.65 ~ p.69
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Gastrointestinal Stromal Tumor Accompanied with von Recklinghausen’s Disease - Positive for CD117, CD34, SMA and S-100 Protein -
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배성우/Bae SW
유진예/문화숙/홍숙희/Yoo JY/Moon HS/Hong SH
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Abstract
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Gastrointestinal stromal tumors (GISTs) are CD117-positive primary mesenchymal tumors of the gastrointestinal tract and they have a characteristic set of morphologic features. GISTs have been noted to have a possible non-random association with neurofibromatosis-1 (NF-1, von Recklinghausen disease). We report here on a case of multiple GISTs with abundant skenoid fiber in the jejunum of a 47-year-old woman, and this condition was accompanied with NF-1. The tumor cells coexpressed smooth muscle actin, S-100 protein, CD117 and CD34. These immunohistochemical results are extremely rare findings for GISTs accompanying with NF-1. We think this is the first report of GISTs arising within NF-1 with the dual immunohistochemical differentiation of neuronal and muscular markers. (J Korean Surg Soc 2006;70:65-69)
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KEYWORD
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